{"id":186,"date":"2017-01-15T22:53:05","date_gmt":"2017-01-15T19:53:05","guid":{"rendered":"http:\/\/werathah.com\/birth-defects\/?p=186"},"modified":"2018-04-04T18:19:34","modified_gmt":"2018-04-04T15:19:34","slug":"usher-syndrome","status":"publish","type":"post","link":"https:\/\/werathah.com\/birth-defects\/genetic-disorders\/usher-syndrome\/","title":{"rendered":"\u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0627\u064f\u0648\u0634\u0631"},"content":{"rendered":"<h1 style=\"text-align: center;\"><span style=\"color: #008000;\"><strong>\u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0627\u064f\u0648\u0634\u0631<\/strong> <\/span><\/h1>\n<h3 style=\"text-align: center;\"><strong>Usher Syndrome<\/strong><\/h3>\n<p>&nbsp;<\/p>\n<p>\u064a\u0635\u064a\u0628 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u062c\u0645\u064a\u0639 \u0627\u0644\u0634\u0639\u0648\u0628 \u0648 \u0644\u0643\u0646 \u0627\u0644\u062f\u0643\u062a\u0648\u0631 \u0627\u0644\u0628\u0631\u0634\u062a \u0641\u0648\u0646 \u062c\u0631\u064a\u0641\u064a(. Albrecht Von Graefe)\u00a0 \u0648\u0635\u0641\u0629 \u0644\u0623\u0648\u0644 \u0645\u0631\u0629 \u0639\u0627\u0645 1858 \u0641\u064a \u0628\u0639\u0636 \u0627\u0644\u064a\u0647\u0648\u062f \u0627\u0644\u0630\u064a\u0646 \u064a\u0642\u0637\u0646\u0648\u0646 \u0639\u0627\u0635\u0645\u0629 \u0627\u0644\u0645\u0627\u0646\u064a\u0627 \u0628\u0631\u0644\u064a\u0646.\u0648 \u0628\u0639\u062f \u0645\u0636\u064a \u062a\u0642\u0631\u064a\u0628\u0627 50 \u0633\u0646\u0629 \u0642\u0627\u0645 \u0637\u0628\u064a\u0628\u00a0 \u0627\u0644\u0639\u064a\u0648\u0646 \u0627\u0644\u062f\u0643\u062a\u0648\u0631 \u0634\u0627\u0631\u0644\u0632 \u0627\u0648\u0634\u0631(Dr. Charles Usher) \u0645\u0646 \u0627\u0646\u062c\u0644\u062a\u0631\u0627 \u0628\u0627\u0643\u062a\u0634\u0627\u0641 \u0627\u0644\u0645\u0631\u0636 \u0639\u0644\u0649 \u0627\u0646\u0647 \u0645\u0631\u0636 \u0648\u0631\u0627\u062b\u064a \u064a\u0646\u062a\u0642\u0644 \u0645\u0646 \u0627\u0644\u0623\u0628\u0648\u064a\u0646 \u0625\u0644\u0649 \u0623\u0648\u0644\u0627\u062f\u0647\u0645.<\/p>\n<p>\u0648 \u0645\u0639 \u0645\u0636\u064a \u0627\u0644\u0648\u0642\u062a \u062a\u0628\u064a\u0646 \u0644\u0644\u0623\u0637\u0628\u0627\u0621 \u0623\u0646 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u064a\u0646\u0642\u0633\u0645 \u0639\u0644\u0649 \u0627\u0644\u0623\u0642\u0644 \u0625\u0644\u0649 3 \u0623\u0646\u0648\u0627\u0639 \u062d\u0633\u0628 \u0634\u062f\u0629 \u0636\u0639\u0641 \u0627\u0644\u0633\u0645\u0639 \u0648 \u0627\u0644\u062a\u0648\u0627\u0632\u0646 \u0648 \u0627\u0644\u0628\u0635\u0631.\u0641\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 (USH1)\u00a0 \u064a\u062a\u0645\u064a\u0632 \u0628\u0635\u0645\u0645 \u0634\u062f\u064a\u062f \u0639\u0646\u062f \u0627\u0644\u0648\u0644\u0627\u062f\u0629 \u0645\u0639 \u0645\u0634\u0643\u0644\u0629 \u0641\u064a \u062d\u0641\u0638 \u0627\u0644\u062a\u0648\u0627\u0632\u0646 \u0648 \u064a\u0628\u062f\u0623 \u0628\u0635\u0631\u0647\u0645 \u064a\u0636\u0639\u0641 \u0628\u0639\u062f \u0628\u0644\u0648\u063a\u0647\u0645 \u0627\u0644\u0633\u0646\u0629 \u0627\u0644\u0639\u0627\u0634\u0631\u0629 \u0645\u0646 \u0627\u0644\u0639\u0645\u0631. \u0628\u064a\u0646\u0645\u0627 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0646\u064a (USH2) \u0641\u064a\u062a\u0645\u064a\u0632 \u0628\u0636\u0639\u0641 \u0633\u0645\u0639 \u0645\u062a\u0648\u0633\u0637 \u0627\u0644\u0634\u062f\u0629 \u0639\u0646\u062f \u0627\u0644\u0648\u0644\u0627\u062f\u0629 \u0648 \u064a\u0628\u062f\u0623 \u0628\u0635\u0631\u0647\u0645 \u0628\u0627\u0644\u0636\u0639\u0641 \u0628\u0639\u062f \u0628\u0644\u0648\u063a\u0647\u0645 20 \u0633\u0646\u0629 \u0648 \u0644\u0627 \u064a\u0639\u0627\u0646\u0648\u0646 \u0645\u0646 \u0645\u0634\u0627\u0643\u0644 \u0641\u064a \u0627\u0644\u062a\u0648\u0627\u0632\u0646 \u0623\u0637\u0644\u0627\u0642\u0627.\u0623\u0645\u0627 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0644\u062b (USH3) \u0641\u064a\u062a\u0645\u064a\u0632 \u0628\u0636\u0639\u0641 \u0633\u0645\u0639 \u062a\u062f\u0631\u064a\u062c\u064a(\u064a\u0636\u0639\u0641 \u0627\u0644\u0633\u0645\u0639 \u0645\u0639 \u0627\u0644\u0648\u0642\u062a) \u0628\u0639\u062f \u0627\u0644\u0628\u062f\u0621 \u0628\u0627\u0644\u0643\u0644\u0627\u0645 \u0648 \u064a\u062e\u062a\u0644\u0641 \u0648\u0642\u062a \u0638\u0647\u0648\u0631 \u0636\u0639\u0641 \u0627\u0644\u0628\u0635\u0631 \u0641\u0642\u062f \u064a\u0638\u0647\u0631 \u0628\u0639\u062f \u0627\u0644\u0633\u0646\u0629 \u0627\u0644\u0639\u0627\u0634\u0631\u0629 \u0623\u0648 \u0627\u0644\u0639\u0634\u0631\u064a\u0646 \u0645\u0646 \u0627\u0644\u0639\u0645\u0631\u060c \u0643\u0645\u0627 \u0623\u0646\u0647\u0645 \u0641\u064a \u0627\u0644\u063a\u0627\u0644\u0628 \u0644\u0627 \u064a\u0639\u0627\u0646\u0648\u0646 \u0645\u0646 \u0645\u0634\u0627\u0643\u0644 \u0641\u064a \u0627\u0644\u0627\u062a\u0632\u0627\u0646.\u0648 \u064a\u0645\u062b\u0644 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u0648 \u0627\u0644\u062b\u0627\u0646\u064a \u0645\u0627 \u0646\u0633\u0628\u0629 90-95% \u0645\u0646 \u062d\u0627\u0644\u0627\u062a \u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0627\u0648\u0634\u0631.<\/p>\n<p>\u0648 \u064a\u0628\u062f\u0623 \u0636\u0639\u0641 \u0627\u0644\u0628\u0635\u0631 \u0628\u0635\u0639\u0648\u0628\u0629 \u0641\u064a \u0627\u0644\u0625\u0628\u0635\u0627\u0631 \u0641\u064a \u0627\u0644\u0644\u064a\u0644(\u0627\u0644\u0639\u0634\u0649 \u0627\u0644\u0644\u064a\u0644\u064a) \u0648 \u062e\u0627\u0635\u0629 \u0645\u062c\u0627\u0644 \u0627\u0644\u0631\u0624\u064a\u0629 \u0627\u0644\u062c\u0627\u0646\u0628\u064a \u062b\u0645 \u064a\u0645\u062a\u062f \u0625\u0644\u0649 \u0623\u0646 \u064a\u0634\u0645\u0644 \u0645\u0631\u0643\u0632 \u0627\u0644\u0628\u0635\u0631 \u0641\u064a \u0627\u0644\u0648\u0633\u0637 \u0648 \u0630\u0644\u0643 \u0646\u062a\u064a\u062c\u0629 \u0644\u0636\u0645\u0648\u0631 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u0628\u0635\u0631\u064a\u0629 \u0641\u064a \u0627\u0644\u0634\u0628\u0643\u064a\u0629.\u0648 \u0646\u0638\u0631\u0627 \u0644\u0635\u0639\u0648\u0628\u0629 \u0645\u0639\u0631\u0641\u0629 \u0627\u0644\u0634\u062e\u0635 \u0627\u0644\u0630\u064a \u0633\u0648\u0641 \u064a\u0635\u0627\u0628 \u0628\u0645\u0634\u0643\u0644\u0629 \u0641\u064a \u0627\u0644\u0628\u0635\u0631 \u0641\u0627\u0646\u0647 \u064a\u0644\u0632\u0645 \u0641\u062d\u0635 \u062c\u0645\u064a\u0639 \u0645\u0646 \u0644\u062f\u064a\u0647\u0645 \u0635\u0645\u0645 \u0623\u0648 \u0636\u0639\u0641 \u0633\u0645\u0639 \u0645\u0646 \u0642\u0628\u0644 \u0637\u0628\u064a\u0628 \u0627\u0644\u0639\u064a\u0648\u0646 \u0644\u0644\u0627\u0643\u062a\u0634\u0627\u0641 \u062a\u0628\u0631\u0642\u0634 \u0627\u0644\u0634\u0628\u0643\u064a\u0629(Retinitis Pigmentosa)\u00a0 \u0645\u0639 \u0625\u062c\u0631\u0627\u0621 \u062a\u062e\u0637\u064a\u0637 \u0644\u0644\u0639\u0635\u0628 \u0627\u0644\u0628\u0635\u0631\u064a(VER) \u0648 \u062a\u062e\u0637\u064a\u0637 \u0644\u0644\u0634\u0628\u0643\u064a\u0629(ERG ). \u0648 \u0625\u0639\u0627\u062f\u062a\u0647\u0627 \u0641\u064a \u0628\u0639\u062f \u0639\u062f\u0629 \u0633\u0646\u0648\u0627\u062a \u0628\u0634\u0643\u0644 \u062f\u0648\u0631\u064a \u062e\u0627\u0635\u0629 \u0641\u064a \u0627\u0644\u0623\u0633\u0631 \u0627\u0644\u062a\u064a \u0644\u062f\u064a\u0647\u0627 \u062a\u0627\u0631\u064a\u062e \u0645\u0631\u0636\u064a \u064a\u0624\u0634\u0631 \u0625\u0644\u0649 \u0625\u0635\u0627\u0628\u0629 \u0627\u0644\u0628\u0635\u0631 \u0645\u0639 \u0627\u0644\u0635\u0645\u0645.\u0643\u0645\u0627 \u064a\u062c\u0631\u0649 \u0627\u062e\u062a\u0628\u0627\u0631 \u0644\u0644\u062a\u0648\u0627\u0632\u0646 Electronystagmography<\/p>\n<p>\u0627\u0644\u062a\u0627\u0631\u064a\u062e \u0645\u0631\u0636\u064a \u064a\u0624\u0634\u0631 \u0625\u0644\u0649 \u0625\u0635\u0627\u0628\u0629 \u0627\u0644\u0628\u0635\u0631 \u0645\u0639 \u0627\u0644\u0635\u0645\u0645.\u0643\u0645\u0627 \u064a\u062c\u0631\u0649 \u0627\u062e\u062a\u0628\u0627\u0631 \u0644\u0644\u062a\u0648\u0627\u0632\u0646 Electronystagmography<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-586\" src=\"http:\/\/werathah.com\/birth-defects\/wp-content\/uploads\/2017\/01\/images-5.jpeg\" alt=\"\" width=\"276\" height=\"183\" srcset=\"https:\/\/werathah.com\/birth-defects\/wp-content\/uploads\/2017\/01\/images-5.jpeg 276w, https:\/\/werathah.com\/birth-defects\/wp-content\/uploads\/2017\/01\/images-5-207x136.jpeg 207w, https:\/\/werathah.com\/birth-defects\/wp-content\/uploads\/2017\/01\/images-5-140x94.jpeg 140w\" sizes=\"auto, (max-width: 276px) 100vw, 276px\" \/><\/p>\n<h2><span style=\"color: #008000;\"><strong>\u0645\u0627\u0647\u064a \u0627\u0644\u0645\u062a\u0644\u0627\u0632\u0645\u0629<\/strong><\/span><\/h2>\n<p>\u062a\u0639\u062a\u0628\u0631 \u0643\u0644\u0645\u0629 \u0645\u062a\u0644\u0627\u0632\u0645\u0629(Syndrome) \u0645\u0646 \u0627\u0644\u0643\u0644\u0645\u0627\u062a \u0627\u0644\u062a\u064a \u064a\u0633\u062a\u062e\u062f\u0645\u0647\u0627\u00a0 \u0627\u0637\u0628\u0627\u0621 \u0627\u0644\u0648\u0631\u0627\u062b\u0629 \u0628\u0634\u0643\u0644 \u0643\u0628\u064a\u0631. \u0648 \u0647\u064a \u0631\u062f\u064a\u0641\u0647 \u0644\u0643\u0644\u0645\u0629 \u0645\u0631\u0636 \u0627\u0648 \u062d\u0627\u0644\u0629. \u0641\u0645\u062b\u0644\u0627 \u064a\u0645\u0643\u0646 \u0627\u0646 \u064a\u0637\u0644\u0642 \u0639\u0644\u0649 \u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0627\u0648\u0634\u0631 \u0645\u0631\u0636 \u0627\u0648 \u0634\u0631 \u0627\u0648 \u062d\u0627\u0644\u0629 \u0627\u0648\u0634\u0631.\u0648\u00a0 \u0641\u064a \u0627\u0644\u0627\u0635\u0644 \u0641\u0627\u0646 \u0643\u0644\u0645\u0629 \u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0645\u0623\u062e\u0648\u0630\u0629 \u0645\u0646 \u0643\u0644\u0645\u0629 &#8220;\u0634\u064a\u0621 \u064a\u0644\u0632\u0645 \u0634\u064a\u0621&#8221; !. \u062d\u064a\u062b \u0625\u0630\u0627 \u0648 \u062c\u062f \u0645\u062b\u0644\u0627 \u0627\u0631\u062a\u062e\u0627\u0621 \u0641\u064a \u0627\u0644\u0639\u0636\u0644\u0627\u062a \u0648 \u0623\u0634\u0628\u0627\u0647 \u0645\u0645\u064a\u0632\u0629 \u0641\u064a \u0627\u0644\u0648\u062c\u0647 \u0641\u0627\u0646\u0647 &#8220;\u064a\u0644\u0632\u0645&#8221; \u0623\u0646 \u064a\u0648\u062c\u062f \u0639\u064a\u0628 \u062e\u0644\u0642\u064a \u0641\u064a \u0627\u0644\u0642\u0644\u0628 \u0648 &#8220;\u064a\u0644\u0632\u0645&#8221; \u0623\u0646 \u064a\u0643\u0648\u0646 \u0647\u0646\u0627\u0643 \u062a\u062e\u0644\u0641 \u0639\u0642\u0644\u064a.\u0648 \u0627\u0644\u0645\u062a\u0644\u0627\u0632\u0645\u0627\u062a \u0643\u062b\u064a\u0631\u0629 \u062c\u062f\u0627 \u0648 \u0644\u0627 \u064a\u0631\u0628\u0637\u0647\u0627 \u0633\u0648\u0649 \u0627\u0644\u0645\u0633\u0645\u0649 \u0641\u0642\u0637 . \u0648 \u062a\u0633\u0645\u0649 \u0627\u0644\u0645\u062a\u0644\u0627\u0632\u0645\u0627\u062a \u0641\u064a \u0627\u0644\u0639\u0627\u062f\u0629 \u0639\u0644\u0649 \u0627\u0633\u0645 \u0627\u0644\u0637\u0628\u064a\u0628 \u0627\u0648 \u0627\u0644\u0623\u0637\u0628\u0627\u0621 \u0627\u0644\u0630\u064a\u0646 \u0627\u0643\u062a\u0634\u0641\u0648\u0647\u0627 \u0623\u0648 \u0646\u0634\u0631\u0648\u0627 \u0639\u0646\u0647\u0627 \u0641\u064a \u0627\u0644\u0645\u062c\u0644\u0627\u062a \u0627\u0644\u0637\u0628\u064a\u0629 \u0648 \u0630\u0644\u0643 \u0644\u0627\u0646 \u0647\u0630\u0647 \u0627\u0644\u0645\u062a\u0644\u0627\u0632\u0645\u0627\u062a \u0644\u0645 \u062a\u0639\u0631\u0641 \u0623\u0633\u0628\u0627\u0628\u0647\u0627 \u0648 \u0644\u0627 \u0645\u0646\u0634\u0626\u0647\u0627 \u0639\u0646\u062f\u0645\u0627 \u0627\u0643\u062a\u0634\u0641\u062a.<\/p>\n<p>\u0648 \u062d\u064a\u062b \u0623\u0646 \u0645\u0634\u0643\u0644\u0629 \u0627\u0644\u062a\u0648\u0627\u0632\u0646 \u0642\u062f \u062a\u0643\u0648\u0646 \u0634\u062f\u064a\u062f\u0629 \u0641\u064a \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u0641\u0627\u0646 \u0627\u0644\u0645\u0635\u0627\u0628\u064a\u0646 \u0628\u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u064a\u062a\u0623\u062e\u0631\u0648\u0646 \u0641\u064a \u0627\u0644\u062c\u0644\u0648\u0633 \u0648 \u0627\u0644\u0645\u0634\u064a \u062d\u064a\u062b \u0627\u0646\u0647 \u064a\u0646\u062f\u0631 \u0623\u0646 \u064a\u0645\u0634\u0648\u0627 \u0642\u0628\u0644 \u0625\u0643\u0645\u0627\u0644\u0647\u0645 18 \u0634\u0647\u0631 \u0645\u0646 \u0627\u0644\u0639\u0645\u0631.<\/p>\n<p>\u0643\u0645\u0627 \u064a\u0643\u0648\u0646 \u0627\u0644\u0635\u0645\u0645 \u0645\u0646 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0634\u062f\u064a\u062f \u0641\u064a \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u0648 \u0641\u064a \u0627\u0644\u0639\u0627\u062f\u0629 \u0644\u0627 \u064a\u0633\u062a\u0641\u064a\u062f\u0648\u0646 \u0645\u0646 \u0633\u0645\u0627\u0639\u0629 \u0627\u0644\u0623\u0630\u0646 \u0648 \u0641\u064a \u0627\u0644\u0646\u0647\u0627\u064a\u0629 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\u0627\u0644\u0623\u0645 \u0646\u0627\u0642\u0644\u064a\u0646(\u062d\u0627\u0645\u0644\u064a\u0646) \u0644\u0644\u0645\u0631\u0636 \u0648 \u064a\u0635\u064a\u0628 25% \u0645\u0646 \u0623\u0648\u0644\u0627\u062f\u0647\u0645. \u0648 \u0644\u0645\u0632\u064a\u062f \u0645\u0646 \u0627\u0644\u0645\u0639\u0644\u0648\u0645\u0627\u062a \u0631\u0627\u062c\u0639 \u0635\u0641\u062d\u0629 \u0627\u0644\u0648\u0631\u0627\u062b\u0629 \u0627\u0644\u0645\u062a\u0646\u062d\u064a\u0629.<\/p>\n<p>\u0648 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0646\u0627\u062a\u062c \u0639\u0646 \u062e\u0644\u0644 \u0641\u064a \u0627\u0644\u062c\u064a\u0646\u0627\u062a. \u0648 \u0644\u0642\u062f \u0627\u0643\u062a\u0634\u0641 \u0625\u0644\u0649 \u0627\u0644\u0622\u0646 7 \u062c\u064a\u0646\u0627\u062a \u0645\u0633\u0628\u0628 \u0644\u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636. 5 \u062c\u064a\u0646\u0627\u062a \u0644\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u0645\u0646 \u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0627\u0648\u0634\u0631( MY07A, USH1C, CDH23, PCDH15,SANS ) \u0648 \u0648\u0627\u062d\u062f \u0644\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0646\u064a(USH2A)\u00a0\u00a0 \u0648 \u0623\u062e\u0631 \u0644\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0644\u062b(USH3A).\u0648 \u064a\u062a\u0648\u0642\u0639 \u0623\u0646 \u0647\u0646\u0627\u0643 \u062c\u064a\u0646\u0627\u062a \u0625\u0636\u0627\u0641\u064a\u0629(\u062a\u0632\u064a\u062f \u0639\u0646 5\u062c\u064a\u0646\u0627\u062a) \u0644\u0645 \u064a\u062a\u0645 \u0627\u0643\u062a\u0634\u0627\u0641\u0647\u0627 \u0625\u0644\u0649 \u0627\u0644\u0622\u0646 \u0648 \u0644\u0643\u0646 \u064a\u062a\u0648\u0642\u0639 \u0623\u0646 \u062a\u0643\u062a\u0634\u0641 \u0641\u064a \u0627\u0644\u0642\u0631\u064a\u0628 \u0627\u0644\u0639\u0627\u062c\u0644.<\/p>\n<p>\u0648 \u0628\u064a\u0646\u0645\u0627 \u0639\u0627\u0644\u0645\u064a\u0627 \u062a\u0645\u062b\u0644 \u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0627\u0648\u0634\u0631 5% \u0625\u0644\u0649 10% \u0645\u0646 \u0645\u062c\u0645\u0648\u0639 \u0645\u0646 \u0644\u062f\u064a\u0647\u0645 \u0635\u0645\u0645 \u0645\u0646\u0630 \u0627\u0644\u0648\u0644\u0627\u062f\u0629 \u0625\u0644\u0627 \u0623\u0646\u0646\u0627 \u0646\u062a\u0648\u0642\u0639 \u0623\u0646 \u0647\u0630\u0647 \u0627\u0644\u0646\u0633\u0628\u0629 \u0623\u0639\u0644\u0649 \u0641\u064a \u0627\u0644\u0634\u0639\u0648\u0628 \u0627\u0644\u0639\u0631\u0628\u064a\u0629 \u0646\u062a\u064a\u062c\u0629 \u0644\u0627\u0631\u062a\u0641\u0627\u0639 \u0632\u0648\u0627\u062c \u0627\u0644\u0623\u0642\u0627\u0631\u0628.<\/p>\n<p>\u0648 \u0645\u0639 \u0623\u0646 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0644\u064a\u0633 \u0644\u0647 \u0639\u0644\u0627\u062c \u0634\u0627\u0641\u064a \u0641\u064a \u0627\u0644\u0648\u0642\u062a \u0627\u0644\u062d\u0627\u0644\u064a \u0625\u0644\u0627 \u0627\u0646\u0647 \u0645\u0646 \u0627\u0644\u0645\u0647\u0645 \u0627\u0643\u062a\u0634\u0627\u0641\u0647\u0627 \u0641\u064a \u0648\u0642\u062a \u0645\u0628\u0643\u0631 \u0642\u0628\u0644 \u0627\u0644\u0625\u0635\u0627\u0628\u0629 \u0628\u0627\u0644\u0639\u0645\u0649 . \u062d\u064a\u062b \u064a\u0645\u0643\u0646 \u0641\u064a \u0630\u0644\u0643 \u0627\u0644\u0648\u0642\u062a \u062a\u062f\u0631\u064a\u0628 \u0645\u0646 \u0644\u062f\u064a\u0647 \u0642\u0627\u0628\u0644\u064a\u0629 \u0623\u0646 \u064a\u0635\u0627\u0628 \u0628\u0627\u0644\u0639\u0645\u0649 \u0644\u0627 \u0642\u062f \u0627\u0644\u0644\u0647 \u0639\u0644\u0649 \u0637\u0631\u0642 \u0627\u0644\u062a\u0648\u0627\u0635\u0644 \u0648 \u0627\u0644\u062a\u062e\u0627\u0637\u0628 \u0628\u0627\u0644\u0645\u0633 \u0648 \u0627\u0644\u0627\u0633\u062a\u062f\u0644\u0627\u0644 \u0627\u0644\u062d\u0631\u0643\u064a(orientation and mobility training) \u0644\u0643\u064a \u064a\u062a\u0623\u0642\u0644\u0645 \u0648 \u064a\u062a\u0639\u0648\u062f \u0639\u0644\u0649 \u0627\u0644\u062d\u0631\u0643\u0629 \u0645\u0639 \u0636\u0639\u0641 \u0627\u0644\u0628\u0635\u0631 \u0648 \u0627\u0644\u0635\u0645\u0645 . \u0648 \u0627\u0644\u062a\u062f\u0631\u064a\u0628 \u0639\u0644\u0649 \u0627\u0644\u0639\u064a\u0634 \u0645\u0646 \u062f\u0648\u0646 \u0627\u0644\u0627\u0639\u062a\u0645\u0627\u062f \u0639\u0644\u0649 \u0627\u0644\u063a\u064a\u0631(independent-living training).\u0648 \u062a\u0648\u0641\u064a\u0631 \u0627\u0644\u0623\u062c\u0647\u0632\u0629 \u0627\u0644\u0645\u0633\u0627\u0646\u062f\u0629 \u0644\u0644\u0633\u0645\u0639(Assistive Listening Devices). \u0643\u0630\u0644\u0643 \u0645\u0633\u0627\u0639\u062f\u062a\u0647 \u0641\u064a \u0623\u0646\u00a0 \u064a\u062e\u062a\u0627\u0631\u00a0 \u0627\u0644\u062f\u0631\u0627\u0633\u0629 \u0627\u0644\u062a\u064a \u062a\u0646\u0627\u0633\u0628\u0647 \u0648 \u0627\u0644\u062a\u064a \u0639\u0644\u0649\u00a0 \u0636\u0648\u0626\u0647\u0627 \u064a\u0633\u062a\u0637\u064a\u0639 \u0623\u0646 \u064a\u062e\u062a\u0627\u0631 \u0627\u0644\u0639\u0645\u0644 \u0627\u0644\u0645\u0646\u0627\u0633\u0628(career counseling) \u0648\u0644\u0627 \u064a\u0634\u062a\u0631\u0637 \u0623\u0628\u0635\u0627\u0631 \u0648 \u0633\u0645\u0639 \u0642\u0648\u064a.\u0643\u0645\u0627 \u0642\u062f \u064a\u0646\u0635\u062d \u0628\u0625\u062c\u0631\u0627\u0621 \u0632\u0631\u0627\u0639\u0629 \u0644\u0644\u0642\u0648\u0642\u0639\u0629 \u0644\u0647\u0630\u0647 \u0627\u0644\u0641\u0626\u0629 \u0644\u0644\u062a\u0642\u0644\u064a\u0644 \u0648\u062c\u0648\u062f \u0625\u0639\u0627\u0642\u062a\u064a\u0646 \u0628\u0635\u0631\u064a\u0629 \u0648 \u0633\u0645\u0639\u064a\u0629.<\/p>\n<p>\u0648 \u0645\u0639 \u0623\u0646 \u0645\u0639\u0638\u0645 \u0645\u0646 \u0644\u062f\u064a\u0647\u0645 \u0647\u0630\u0647 \u0627\u0644\u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0644\u0627 \u064a\u0639\u0627\u0646\u0648\u0646 \u0645\u0646 \u0645\u0634\u0627\u0643\u0644 \u0639\u0642\u0644\u064a\u0629 \u0625\u0644\u0627 \u0623\u0646 \u0646\u0633\u0628\u0629 \u0642\u0644\u064a\u0644\u0629 \u0645\u0646\u0647\u0645 \u0644\u062f\u064a\u0647 \u0635\u0639\u0648\u0628\u0627\u062a \u062a\u0639\u0644\u0645 \u0623\u0648 \u062a\u0623\u062e\u0631 \u0639\u0642\u0644\u064a \u0628\u0633\u064a\u0637 \u0623\u0648 \u062a\u0648\u062d\u062f \u0648 \u0647\u0624\u0644\u0627\u0621 \u064a\u062d\u062a\u0627\u062c\u0648\u0646 \u0644\u0631\u0639\u0627\u064a\u0629 \u062f\u0642\u064a\u0642\u0629 \u0644\u0643\u064a \u064a\u062a\u062c\u0627\u0648\u0632\u0648\u0627 \u0647\u0630\u0647 \u0627\u0644\u0645\u0634\u0643\u0644\u0627\u062a \u0648 \u0630\u0644\u0643 \u0628\u0625\u0639\u062f\u0627\u062f \u0628\u0631\u0646\u0627\u0645\u062c \u062a\u062f\u0631\u064a\u0628\u064a \u0644\u062a\u0623\u0647\u064a\u0644\u0647\u0645 \u0648 \u062a\u0639\u0644\u064a\u0645\u0647\u0645.<\/p>\n<h2 style=\"text-align: right;\"><span style=\"color: #008000;\"><strong>\u062a\u0623\u0644\u064a\u0641 : \u0627\u0644\u062f\u0643\u062a\u0648\u0631 \u0639\u0628\u062f\u0627\u0644\u0631\u062d\u0645\u0646 \u0627\u0644\u0633\u0648\u064a\u062f<\/strong><\/span><\/h2>\n<h2 style=\"text-align: right;\"><span style=\"color: #008000;\"><strong>\u0627\u0633\u062a\u0634\u0627\u0631\u064a \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629 \u0648 \u0637\u0628 \u0627\u0644\u0623\u0637\u0641\u0627\u0644<\/strong><\/span><\/h2>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>\u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0627\u064f\u0648\u0634\u0631 Usher Syndrome &nbsp; \u064a\u0635\u064a\u0628 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u062c\u0645\u064a\u0639 \u0627\u0644\u0634\u0639\u0648\u0628 \u0648 \u0644\u0643\u0646 \u0627\u0644\u062f\u0643\u062a\u0648\u0631 \u0627\u0644\u0628\u0631\u0634\u062a \u0641\u0648\u0646 \u062c\u0631\u064a\u0641\u064a(. Albrecht Von Graefe)\u00a0 \u0648\u0635\u0641\u0629 \u0644\u0623\u0648\u0644 \u0645\u0631\u0629 \u0639\u0627\u0645 1858 \u0641\u064a \u0628\u0639\u0636 \u0627\u0644\u064a\u0647\u0648\u062f \u0627\u0644\u0630\u064a\u0646 \u064a\u0642\u0637\u0646\u0648\u0646 \u0639\u0627\u0635\u0645\u0629 \u0627\u0644\u0645\u0627\u0646\u064a\u0627 \u0628\u0631\u0644\u064a\u0646.\u0648 \u0628\u0639\u062f \u0645\u0636\u064a \u062a\u0642\u0631\u064a\u0628\u0627 50 \u0633\u0646\u0629 \u0642\u0627\u0645 \u0637\u0628\u064a\u0628\u00a0 \u0627\u0644\u0639\u064a\u0648\u0646 \u0627\u0644\u062f\u0643\u062a\u0648\u0631 \u0634\u0627\u0631\u0644\u0632 \u0627\u0648\u0634\u0631(Dr. Charles Usher) \u0645\u0646 \u0627\u0646\u062c\u0644\u062a\u0631\u0627 \u0628\u0627\u0643\u062a\u0634\u0627\u0641 \u0627\u0644\u0645\u0631\u0636 \u0639\u0644\u0649 \u0627\u0646\u0647 \u0645\u0631\u0636 \u0648\u0631\u0627\u062b\u064a \u064a\u0646\u062a\u0642\u0644 \u0645\u0646 &hellip;<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[7,10],"tags":[80,54,55,87,82,77,60,81,67,88,72,71,74,58,57,61,83,59,53,63,86,64,73,69,66,84,75,76,70,79,56,68,85,51,52,62,65,115,78,19,20,15,31,43,40,23,42,41,18,29,14,30,39,37,24,34,12,21,16,38,32,48,45,114,33,46,17,25,36,22,50,11,47,44,28,35,27,49,13,26],"class_list":["post-186","post","type-post","status-publish","format-standard","hentry","category-genetic-disorders","category-deafness","tag-amniocentesis","tag-arabic","tag-arabica","tag-birth","tag-blood","tag-chorionic","tag-chromosome","tag-cord","tag-deafness","tag-defects","tag-delay","tag-developmental","tag-diagnosis","tag-disease","tag-disorder","tag-dna","tag-fetus","tag-gene","tag-genetic","tag-geneticist","tag-group","tag-hospital","tag-investigation","tag-mental","tag-neurology","tag-newborn","tag-preimplantation","tag-prenatal","tag-retardation","tag-sampling","tag-saudi","tag-seizure","tag-support","tag-syndrome","tag-syndromes","tag-testing","tag-treatment","tag-usher","tag-villus","tag-19","tag-20","tag-15","tag-31","tag-43","tag-40","tag-23","tag-42","tag-41","tag-18","tag-29","tag-14","tag-30","tag-39","tag-37","tag-24","tag-34","tag-12","tag-21","tag-16","tag-38","tag-32","tag-48","tag-45","tag-114","tag-33","tag-46","tag-17","tag-25","tag-36","tag-22","tag-50","tag-11","tag-47","tag-44","tag-28","tag-35","tag-27","tag-49","tag-13","tag-26"],"_links":{"self":[{"href":"https:\/\/werathah.com\/birth-defects\/wp-json\/wp\/v2\/posts\/186","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/werathah.com\/birth-defects\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/werathah.com\/birth-defects\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/werathah.com\/birth-defects\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/werathah.com\/birth-defects\/wp-json\/wp\/v2\/comments?post=186"}],"version-history":[{"count":0,"href":"https:\/\/werathah.com\/birth-defects\/wp-json\/wp\/v2\/posts\/186\/revisions"}],"wp:attachment":[{"href":"https:\/\/werathah.com\/birth-defects\/wp-json\/wp\/v2\/media?parent=186"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/werathah.com\/birth-defects\/wp-json\/wp\/v2\/categories?post=186"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/werathah.com\/birth-defects\/wp-json\/wp\/v2\/tags?post=186"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}